Von Hippel-Lindau Disease

Definition

Von Hippel-Lindau disease is an inherited syndrome characterized by benign and malignant tumors in multiple organs.

Symptoms

  • Retinal hemangioblastoma
  • Cerebellar hemangioblastoma
  • Kidney carcinoma
  • Pheochromocytoma

Reasons

VHL gene mutation.

Diagnosis

Clinical criteria, genetic testing.

Treatment

Surgery, radiosurgery.

Which Polyclinic Should You Apply To?

Genetics Polyclinic

What to Do in an Emergency?

In case of neurological deficit, emergency services should be consulted.

This page is for general information purposes only.