Thrombotic Thrombocytopenic Purpura

Definition

Thrombotic thrombocytopenic purpura is a life-threatening disease characterized by microangiopathic hemolytic anemia and thrombocytopenia.

Symptoms

  • Neurological findings
  • Fire
  • Kidney failure
  • Bleeding

Reasons

ADAMTS13 enzyme deficiency.

Diagnosis

Peripheral smear, ADAMTS13 activity.

Treatment

Plasma exchange, immunosuppressives.

Which Polyclinic Should You Apply To?

Hematology Polyclinic

What to Do in an Emergency?

In case of neurological findings, emergency services should be consulted immediately.

This page is for general information purposes only.