Refsum Disease

Definition

Refsum disease is a rare metabolic disease characterized by retinitis pigmentosa, ataxia and peripheral neuropathy, resulting from phytanic acid accumulation.

Symptoms

  • Retinitis pigmentosa
  • Ataxia
  • Peripheral neuropathy
  • Hearing loss

Reasons

PHYH or PEX7 gene mutations.

Diagnosis

Plasma phytanic acid level.

Treatment

Dietary restriction.

Which Polyclinic Should You Apply To?

Metabolism Polyclinic

What to Do in an Emergency?

In case of cardiac arrhythmia, emergency services should be consulted.

This page is for general information purposes only.