Rabson-Mendenhall Syndrome

Definition

Rabson-Mendenhall syndrome is a rare genetic disease characterized by severe insulin resistance, dental anomalies, pineal hyperplasia and signs of premature aging.

Symptoms

  • Severe insulin resistance
  • Early tooth decay
  • Pineal gland hyperplasia
  • Acanthosis nigricans

Reasons

Insulin receptor gene (INSR) mutations.

Diagnosis

Clinical findings, high insulin levels, genetic testing.

Treatment

Insulin resistance treatment, dental care, symptomatic treatment.

Which Polyclinic Should You Apply To?

Endocrinology Polyclinic

What to Do in an Emergency?

In case of diabetic ketoacidosis, emergency services should be consulted.

This page is for general information purposes only.