Pyknodysostosis

Definition

Pyknodysostosis is a rare bone disease characterized by short stature, brittle bones, and a characteristic facial appearance.

Symptoms

  • Short stature
  • Brittle bones
  • Characteristic face
  • Osteosclerosis

Reasons

CTSK gene mutation.

Diagnosis

Clinical findings, genetic testing.

Treatment

Symptomatic treatment.

Which Polyclinic Should You Apply To?

Orthopedic Polyclinic

What to Do in an Emergency?

In case of bone fracture, emergency services should be consulted.

This page is for general information purposes only.