Paroxysmal Nocturnal Hemoglobinuria

Definition

Paroxysmal nocturnal hemoglobinuria is a rare disease characterized by complement-mediated hemolysis due to PIG-A gene mutation.

Symptoms

  • Dark urine
  • Weakness
  • Stomach ache
  • Headache

Reasons

PIG-A gene mutation.

Diagnosis

Flow cytometry, LDH, haptoglobin.

Treatment

Eculizumab, corticosteroids, stem cell transplantation.

Which Polyclinic Should You Apply To?

Hematology Polyclinic

What to Do in an Emergency?

In case of severe hemolysis, emergency services should be consulted.

This page is for general information purposes only.