Metatropic Dysplasia

Definition

Metatropic dysplasia is a rare skeletal dysplasia characterized by progressive shortening, platyspondyly, and characteristic bone changes.

Symptoms

  • Progressive shortening
  • Platyspondylosis
  • Short rib cage
  • Limited joint movement

Reasons

TRPV4 gene mutation.

Diagnosis

Clinical findings, genetic testing.

Treatment

Orthopedic treatment.

Which Polyclinic Should You Apply To?

Orthopedic Polyclinic

What to Do in an Emergency?

In case of respiratory distress, emergency services should be consulted.

This page is for general information purposes only.