Metachromatic Leukodystrophy

Definition

Metachromatic leukodystrophy is a lysosomal storage disease characterized by progressive neurological impairment and demyelination, resulting from arylsulfatase A enzyme deficiency.

Symptoms

  • Gait disturbance
  • Cognitive decline
  • Peripheral neuropathy
  • Dementia

Reasons

ARSA gene mutation.

Diagnosis

Enzyme activity, genetic testing.

Treatment

Bone marrow transplant.

Which Polyclinic Should You Apply To?

Metabolism Polyclinic

What to Do in an Emergency?

In case of status epilepticus, emergency services should be consulted.

This page is for general information purposes only.