Mucopolysaccharidosis Type VI (Maroteaux-Lamy Syndrome)

Definition

Mucopolysaccharidosis type VI is a lysosomal storage disease characterized by arylsulfatase B enzyme deficiency, skeletal anomalies, and corneal opacity.

Symptoms

  • Skeletal anomalies
  • Corneal opacity
  • Cardiac involvement
  • Normal intelligence

Reasons

ARSB gene mutation.

Diagnosis

Urine GAG, enzyme activity.

Treatment

Enzyme replacement therapy.

Which Polyclinic Should You Apply To?

Metabolism Polyclinic

What to Do in an Emergency?

In case of respiratory distress, emergency services should be consulted.

This page is for general information purposes only.