Oculocerebrorenal Syndrome (Lowe Syndrome)

Definition

Lowe syndrome is an X-linked recessive disorder characterized by congenital cataracts, renal tubular acidosis, and neurological disorders.

Symptoms

  • Congenital cataracts
  • Renal tubular acidosis
  • Developmental delay
  • Hypotonia

Reasons

OCRL gene mutation.

Diagnosis

Clinical findings, genetic testing.

Treatment

Multidisciplinary approach.

Which Polyclinic Should You Apply To?

Metabolism Polyclinic

What to Do in an Emergency?

In case of metabolic acidosis, emergency services should be consulted.

This page is for general information purposes only.