Leigh Syndrome

Definition

Leigh syndrome is a mitochondrial disease characterized by progressive neurological impairment, lactic acidosis, and brainstem involvement.

Symptoms

  • Neurological decline
  • Lactic acidosis
  • Nystagmus
  • Respiratory Failure

Reasons

Various mitochondrial enzyme defects.

Diagnosis

Brain MRI, lactate level, genetic testing.

Treatment

Symptomatic treatment.

Which Polyclinic Should You Apply To?

Metabolism Polyclinic

What to Do in an Emergency?

In case of respiratory failure, emergency services should be consulted.

This page is for general information purposes only.