Kniest Dysplasia

Definition

Kniest dysplasia is a rare skeletal dysplasia characterized by short stature, joint contractures, and characteristic facial appearance.

Symptoms

  • Short stature
  • Joint contractures
  • Characteristic face
  • Myopia

Reasons

COL2A1 gene mutation.

Diagnosis

Clinical findings, genetic testing.

Treatment

Orthopedic treatment.

Which Polyclinic Should You Apply To?

Orthopedic Polyclinic

What to Do in an Emergency?

In case of respiratory distress, emergency services should be consulted.

This page is for general information purposes only.