Mucopolysaccharidosis Type II (Hunter Syndrome)

Definition

Mucopolysaccharidosis type II is an X-linked recessive lysosomal storage disease that develops as a result of iduronate-2-sulfatase enzyme deficiency.

Symptoms

  • Rough facial appearance
  • Skeletal anomalies
  • Behavioral problems
  • Hearing loss

Reasons

IDS gene mutation.

Diagnosis

Urine GAG, enzyme activity.

Treatment

Enzyme replacement therapy.

Which Polyclinic Should You Apply To?

Metabolism Polyclinic

What to Do in an Emergency?

In case of respiratory distress, emergency services should be consulted.

This page is for general information purposes only.