Homocystinuria

Definition

Homocystinuria is a metabolic disease characterized by methionine metabolism disorders, lens dislocation, thromboembolic events and mental retardation.

Symptoms

  • Lens dislocation
  • Thromboembolic events
  • Mental retardation
  • Osteoporosis

Reasons

CBS gene mutation.

Diagnosis

Plasma homocysteine, genetic testing.

Treatment

Pyridoxine, betaine, diet.

Which Polyclinic Should You Apply To?

Metabolism Polyclinic

What to Do in an Emergency?

In case of thromboembolic event, emergency services should be consulted.

This page is for general information purposes only.