Hemophilia B

Definition

Hemophilia B is an X-linked recessive bleeding disorder resulting from factor IX deficiency.

Symptoms

  • Intra-articular hemorrhages
  • Intramuscular bleeding
  • Spontaneous bleeding
  • Prolonged bleeding after surgery

Reasons

Factor IX gene mutation.

Diagnosis

Coagulation tests, factor IX level.

Treatment

Factor IX concentrates.

Which Polyclinic Should You Apply To?

Hematology Polyclinic

What to Do in an Emergency?

In case of severe bleeding, emergency services should be consulted.

This page is for general information purposes only.