Hereditary Fructose Intolerance

Definition

Hereditary fructose intolerance is a metabolic disease characterized by aldolase B enzyme deficiency, which progresses with hypoglycemia and liver failure after fructose intake.

Symptoms

  • Hypoglycemia
  • Stomach ache
  • Vomiting
  • Liver failure

Reasons

ALDOB gene mutation.

Diagnosis

Genetic testing, fructose loading test.

Treatment

Avoiding fructose, sucrose and sorbitol.

Which Polyclinic Should You Apply To?

Metabolism Polyclinic

What to Do in an Emergency?

In case of hypoglycemia, emergency services should be consulted.

This page is for general information purposes only.