Phenylketonuria

Definition

Phenylketonuria is a metabolic disease characterized by phenylalanine hydroxylase enzyme deficiency, accompanied by mental retardation and neurological disorders.

Symptoms

  • Mental retardation
  • Neurological disorder
  • Hypopigmentation
  • Eczematous rash

Reasons

PAH gene mutation.

Diagnosis

Newborn screening, genetic testing.

Treatment

Low phenylalanine diet.

Which Polyclinic Should You Apply To?

Metabolism Polyclinic

What to Do in an Emergency?

In case of metabolic crisis, emergency services should be consulted.

This page is for general information purposes only.