Cutis Laxa

Definition

Cutis laxa is a rare connective tissue disease characterized by sagging and lax skin, pulmonary emphysema, and cardiovascular anomalies.

Symptoms

  • Sagging skin
  • Pulmonary emphysema
  • Cardiovascular anomalies
  • Hernias

Reasons

ELN, FBLN5 gene mutations.

Diagnosis

Clinical findings, genetic testing.

Treatment

Symptomatic treatment.

Which Polyclinic Should You Apply To?

Dermatology Polyclinic

What to Do in an Emergency?

In case of respiratory failure, emergency services should be consulted.

This page is for general information purposes only.