Glycogen Storage Disease Type III (Cori)

Definition

Glycogen storage disease type III is a metabolic disease characterized by debranching enzyme deficiency, hepatomegaly, and myopathy.

Symptoms

  • Hepatomegaly
  • Hypoglycemia
  • Myopathy
  • Growth retardation

Reasons

AGL gene mutation.

Diagnosis

Liver biopsy, genetic testing.

Treatment

High protein diet.

Which Polyclinic Should You Apply To?

Metabolism Polyclinic

What to Do in an Emergency?

In case of hypoglycemia, emergency services should be consulted.

This page is for general information purposes only.