Aarskog-Scott Syndrome

Definition

Aarskog-Scott syndrome is a rare X-linked recessive genetic syndrome characterized by facial, skeletal and genital anomalies.

Symptoms

  • Round face, hypertelorism
  • Short stature
  • Severe craniofacial and skeletal anomalies
  • Genital anomalies (scrotal cap)

Reasons

Mutation in the FGD1 gene.

Diagnosis

Clinical findings, genetic testing.

Treatment

Orthopedic and craniofacial surgery, supportive care.

Which Polyclinic Should You Apply To?

Genetics Polyclinic or Pediatrics Polyclinic

What to Do in an Emergency?

In case of respiratory distress or severe feeding problems, emergency services should be consulted.

This page is for general information purposes only.