{"id":21262,"date":"2025-11-17T01:45:43","date_gmt":"2025-11-16T22:45:43","guid":{"rendered":"https:\/\/hastane.ksu.edu.tr\/hastaliklar\/fruktoz-bifosfataz\/"},"modified":"2025-11-17T01:45:43","modified_gmt":"2025-11-16T22:45:43","slug":"fruktoz-bifosfataz","status":"publish","type":"hastaliklar","link":"https:\/\/hastane.ksu.edu.tr\/en\/hastaliklar\/fruktoz-bifosfataz\/","title":{"rendered":"Fructose-1,6-bisphosphatase Deficiency"},"content":{"rendered":"<h2>Definition<\/h2>\n<p>Fructose-1,6-bisphosphatase deficiency is a metabolic disease characterized by impaired gluconeogenesis and accompanied by hypoglycemia and metabolic acidosis.<\/p>\n<h2>Symptoms<\/h2>\n<ul>\n<li>Hypoglycemia<\/li>\n<li>Lactic acidosis<\/li>\n<li>Hyperventilation<\/li>\n<li>Hepatomegaly<\/li>\n<\/ul>\n<h2>Reasons<\/h2>\n<p>FBP1 gene mutation.<\/p>\n<h2>Diagnosis<\/h2>\n<p>Genetic testing, metabolic testing.<\/p>\n<h2>Treatment<\/h2>\n<p>Frequent feeding, fructose restriction.<\/p>\n<h2>Which Polyclinic Should You Apply To?<\/h2>\n<p><strong>Metabolism Polyclinic<\/strong><\/p>\n<h2>What to Do in an Emergency?<\/h2>\n<p>In case of metabolic acidosis, emergency services should be consulted.<\/p>\n<p><em>This page is for general information purposes only.<\/em><\/p>","protected":false},"excerpt":{"rendered":"<p>Definition: Fructose-1,6-bisphosphatase deficiency is a metabolic disease characterized by impaired gluconeogenesis, resulting in hypoglycemia and metabolic acidosis. Symptoms: Hypoglycemia, lactic acidosis, hyperventilation, hepatomegaly. Causes: FBP1 gene mutation. Diagnosis: Genetic testing, metabolic tests. Treatment: Frequent feeding, fructose restriction. Which Clinic Should You Go To? Metabolism Clinic. What to Do in an Emergency? In case of metabolic acidosis, you should go to the emergency room. This page provides general information [\u2026]<\/p>","protected":false},"author":1,"featured_media":0,"menu_order":0,"template":"","format":"standard","meta":{"_acf_changed":false,"slim_seo":{"title":"Fructose-1,6-bisphosphatase Deficiency - Kahramanmara\u015f S\u00fct\u00e7\u00fc \u0130mam University Health Practice and Research Hospital","description":"Definition: Fructose-1,6-bisphosphatase deficiency is a metabolic disorder characterized by impaired gluconeogenesis, resulting in hypoglycemia and metabolic acidosis. Symptoms"},"footnotes":""},"class_list":["post-21262","hastaliklar","type-hastaliklar","status-publish","format-standard","hentry"],"acf":[],"_links":{"self":[{"href":"https:\/\/hastane.ksu.edu.tr\/en\/wp-json\/wp\/v2\/hastaliklar\/21262","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/hastane.ksu.edu.tr\/en\/wp-json\/wp\/v2\/hastaliklar"}],"about":[{"href":"https:\/\/hastane.ksu.edu.tr\/en\/wp-json\/wp\/v2\/types\/hastaliklar"}],"author":[{"embeddable":true,"href":"https:\/\/hastane.ksu.edu.tr\/en\/wp-json\/wp\/v2\/users\/1"}],"version-history":[{"count":0,"href":"https:\/\/hastane.ksu.edu.tr\/en\/wp-json\/wp\/v2\/hastaliklar\/21262\/revisions"}],"wp:attachment":[{"href":"https:\/\/hastane.ksu.edu.tr\/en\/wp-json\/wp\/v2\/media?parent=21262"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}