{"id":21257,"date":"2025-11-17T01:45:43","date_gmt":"2025-11-16T22:45:43","guid":{"rendered":"https:\/\/hastane.ksu.edu.tr\/hastaliklar\/tarui\/"},"modified":"2025-11-17T01:45:43","modified_gmt":"2025-11-16T22:45:43","slug":"tarui","status":"publish","type":"hastaliklar","link":"https:\/\/hastane.ksu.edu.tr\/en\/hastaliklar\/tarui\/","title":{"rendered":"Glycogen Storage Disease Type VII (Tarui)"},"content":{"rendered":"<h2>Definition<\/h2>\n<p>Glycogen storage disease type VII is a metabolic disease characterized by phosphofructokinase enzyme deficiency, exercise intolerance, and hemolytic anemia.<\/p>\n<h2>Symptoms<\/h2>\n<ul>\n<li>Exercise intolerance<\/li>\n<li>Muscle pain<\/li>\n<li>Hemolytic anemia<\/li>\n<li>Hyperuricemia<\/li>\n<\/ul>\n<h2>Reasons<\/h2>\n<p>PFKM gene mutation.<\/p>\n<h2>Diagnosis<\/h2>\n<p>Muscle biopsy, genetic testing.<\/p>\n<h2>Treatment<\/h2>\n<p>Exercise restriction.<\/p>\n<h2>Which Polyclinic Should You Apply To?<\/h2>\n<p><strong>Metabolism Polyclinic<\/strong><\/p>\n<h2>What to Do in an Emergency?<\/h2>\n<p>In case of myoglobinuria, emergency services should be consulted.<\/p>\n<p><em>This page is for general information purposes only.<\/em><\/p>","protected":false},"excerpt":{"rendered":"<p>Definition: Glycogen storage disease type VII is a metabolic disease characterized by phosphofructokinase enzyme deficiency, exercise intolerance, and hemolytic anemia. Symptoms: Exercise intolerance, muscle pain, hemolytic anemia, hyperuricemia. Causes: PFKM gene mutation. Diagnosis: Muscle biopsy, genetic testing. Treatment: Exercise restriction. Which Clinic Should You Go To? Metabolism Clinic. What to Do in an Emergency? In case of myoglobinuria, go to the emergency room. [\u2026]<\/p>","protected":false},"author":1,"featured_media":0,"menu_order":0,"template":"","format":"standard","meta":{"_acf_changed":false,"slim_seo":{"title":"Glycogen Storage Disease Type VII (Tarui) - Kahramanmara\u015f S\u00fct\u00e7\u00fc \u0130mam University Health Practice and Research Hospital","description":"Definition: Glycogen storage disease type VII is a metabolic disorder characterized by phosphofructokinase enzyme deficiency, exercise intolerance, and hemolytic anemia."},"footnotes":""},"class_list":["post-21257","hastaliklar","type-hastaliklar","status-publish","format-standard","hentry"],"acf":[],"_links":{"self":[{"href":"https:\/\/hastane.ksu.edu.tr\/en\/wp-json\/wp\/v2\/hastaliklar\/21257","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/hastane.ksu.edu.tr\/en\/wp-json\/wp\/v2\/hastaliklar"}],"about":[{"href":"https:\/\/hastane.ksu.edu.tr\/en\/wp-json\/wp\/v2\/types\/hastaliklar"}],"author":[{"embeddable":true,"href":"https:\/\/hastane.ksu.edu.tr\/en\/wp-json\/wp\/v2\/users\/1"}],"version-history":[{"count":0,"href":"https:\/\/hastane.ksu.edu.tr\/en\/wp-json\/wp\/v2\/hastaliklar\/21257\/revisions"}],"wp:attachment":[{"href":"https:\/\/hastane.ksu.edu.tr\/en\/wp-json\/wp\/v2\/media?parent=21257"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}