{"id":21251,"date":"2025-11-17T01:45:43","date_gmt":"2025-11-16T22:45:43","guid":{"rendered":"https:\/\/hastane.ksu.edu.tr\/hastaliklar\/von-gierke\/"},"modified":"2025-11-17T01:45:43","modified_gmt":"2025-11-16T22:45:43","slug":"von-gierke","status":"publish","type":"hastaliklar","link":"https:\/\/hastane.ksu.edu.tr\/en\/hastaliklar\/von-gierke\/","title":{"rendered":"Glycogen Storage Disease Type I (Von Gierke)"},"content":{"rendered":"<h2>Definition<\/h2>\n<p>Glycogen storage disease type I is a metabolic disease characterized by glucose-6-phosphatase enzyme deficiency and characterized by hypoglycemia, hepatomegaly and lactic acidosis.<\/p>\n<h2>Symptoms<\/h2>\n<ul>\n<li>Hypoglycemia<\/li>\n<li>Hepatomegaly<\/li>\n<li>Lactic acidosis<\/li>\n<li>Growth retardation<\/li>\n<\/ul>\n<h2>Reasons<\/h2>\n<p>G6PC gene mutation.<\/p>\n<h2>Diagnosis<\/h2>\n<p>Liver biopsy, genetic testing.<\/p>\n<h2>Treatment<\/h2>\n<p>Frequent feeding, corn starch.<\/p>\n<h2>Which Polyclinic Should You Apply To?<\/h2>\n<p><strong>Metabolism Polyclinic<\/strong><\/p>\n<h2>What to Do in an Emergency?<\/h2>\n<p>In case of hypoglycemia, emergency services should be consulted.<\/p>\n<p><em>This page is for general information purposes only.<\/em><\/p>","protected":false},"excerpt":{"rendered":"<p>Definition: Glycogen storage disease type I is a metabolic disease characterized by glucose-6-phosphatase enzyme deficiency, resulting in hypoglycemia, hepatomegaly, and lactic acidosis. Symptoms: Hypoglycemia, Hepatomegaly, Lactic acidosis, Growth retardation. Causes: G6PC gene mutation. Diagnosis: Liver biopsy, genetic testing. Treatment: Frequent feeding, cornstarch. Which Clinic Should You Go To? Metabolism Clinic. What to Do in an Emergency? In case of hypoglycemia, go to the emergency room [\u2026]<\/p>","protected":false},"author":1,"featured_media":0,"menu_order":0,"template":"","format":"standard","meta":{"_acf_changed":false,"slim_seo":{"title":"Glycogen Storage Disease Type I (Von Gierke) - Kahramanmara\u015f S\u00fct\u00e7\u00fc \u0130mam University Health Practice and Research Hospital","description":"Definition: Glycogen storage disease type I is a metabolic disorder characterized by glucose-6-phosphatase enzyme deficiency, resulting in hypoglycemia, hepatomegaly, and lactic acidosis."},"footnotes":""},"class_list":["post-21251","hastaliklar","type-hastaliklar","status-publish","format-standard","hentry"],"acf":[],"_links":{"self":[{"href":"https:\/\/hastane.ksu.edu.tr\/en\/wp-json\/wp\/v2\/hastaliklar\/21251","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/hastane.ksu.edu.tr\/en\/wp-json\/wp\/v2\/hastaliklar"}],"about":[{"href":"https:\/\/hastane.ksu.edu.tr\/en\/wp-json\/wp\/v2\/types\/hastaliklar"}],"author":[{"embeddable":true,"href":"https:\/\/hastane.ksu.edu.tr\/en\/wp-json\/wp\/v2\/users\/1"}],"version-history":[{"count":0,"href":"https:\/\/hastane.ksu.edu.tr\/en\/wp-json\/wp\/v2\/hastaliklar\/21251\/revisions"}],"wp:attachment":[{"href":"https:\/\/hastane.ksu.edu.tr\/en\/wp-json\/wp\/v2\/media?parent=21251"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}