{"id":21233,"date":"2025-11-17T01:45:43","date_gmt":"2025-11-16T22:45:43","guid":{"rendered":"https:\/\/hastane.ksu.edu.tr\/hastaliklar\/adrenolokodistrofi\/"},"modified":"2025-11-17T01:45:43","modified_gmt":"2025-11-16T22:45:43","slug":"adrenolokodistrofi","status":"publish","type":"hastaliklar","link":"https:\/\/hastane.ksu.edu.tr\/en\/hastaliklar\/adrenolokodistrofi\/","title":{"rendered":"Adrenoleukodystrophy"},"content":{"rendered":"<h2>Definition<\/h2>\n<p>Adrenoleukodystrophy is an X-linked recessive metabolic disease characterized by adrenal insufficiency and progressive neurological impairment.<\/p>\n<h2>Symptoms<\/h2>\n<ul>\n<li>Adrenal insufficiency<\/li>\n<li>Neurological decline<\/li>\n<li>Vision and hearing loss<\/li>\n<li>Behavioral changes<\/li>\n<\/ul>\n<h2>Reasons<\/h2>\n<p>ABCD1 gene mutation.<\/p>\n<h2>Diagnosis<\/h2>\n<p>Plasma very long chain fatty acids, genetic testing.<\/p>\n<h2>Treatment<\/h2>\n<p>Lorenzo&#039;s fat, bone marrow transplant.<\/p>\n<h2>Which Polyclinic Should You Apply To?<\/h2>\n<p><strong>Metabolism Polyclinic<\/strong><\/p>\n<h2>What to Do in an Emergency?<\/h2>\n<p>In case of adrenal crisis, emergency services should be consulted.<\/p>\n<p><em>This page is for general information purposes only.<\/em><\/p>","protected":false},"excerpt":{"rendered":"<p>Definition: Adrenoleukodystrophy is an X-linked recessive metabolic disease characterized by adrenal insufficiency and progressive neurological impairment. Symptoms: Adrenal insufficiency, Neurological regression, Vision and hearing loss, Behavioral changes. Causes: ABCD1 gene mutation. Diagnosis: Plasma very long-chain fatty acids, genetic testing. Treatment: Lorenzo&#039;s fat, bone marrow transplant. Which Clinic Should You Go To? Metabolism Clinic. What to Do in an Emergency? [\u2026]<\/p>","protected":false},"author":1,"featured_media":0,"menu_order":0,"template":"","format":"standard","meta":{"_acf_changed":false,"slim_seo":{"title":"Adrenoleukodystrophy - Kahramanmara\u015f S\u00fct\u00e7\u00fc \u0130mam University Health Practice and Research Hospital","description":"Definition: Adrenoleukodystrophy is an X-linked recessive metabolic disease characterized by adrenal insufficiency and progressive neurological impairment. Symptoms: Adrenal insufficiency"},"footnotes":""},"class_list":["post-21233","hastaliklar","type-hastaliklar","status-publish","format-standard","hentry"],"acf":[],"_links":{"self":[{"href":"https:\/\/hastane.ksu.edu.tr\/en\/wp-json\/wp\/v2\/hastaliklar\/21233","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/hastane.ksu.edu.tr\/en\/wp-json\/wp\/v2\/hastaliklar"}],"about":[{"href":"https:\/\/hastane.ksu.edu.tr\/en\/wp-json\/wp\/v2\/types\/hastaliklar"}],"author":[{"embeddable":true,"href":"https:\/\/hastane.ksu.edu.tr\/en\/wp-json\/wp\/v2\/users\/1"}],"version-history":[{"count":0,"href":"https:\/\/hastane.ksu.edu.tr\/en\/wp-json\/wp\/v2\/hastaliklar\/21233\/revisions"}],"wp:attachment":[{"href":"https:\/\/hastane.ksu.edu.tr\/en\/wp-json\/wp\/v2\/media?parent=21233"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}